CTEPH is a form of pulmonary hypertension caused by blood clots that get stuck in the pulmonary arteries. These clots block blood flow, build pressure, and can cause scar tissue that narrows the arteries further. Symptoms include shortness of breath, weakness, and chest pain.
The good news? CTEPH is one of the few forms of Show Full Answer
CTEPH is a form of pulmonary hypertension caused by blood clots that get stuck in the pulmonary arteries. These clots block blood flow, build pressure, and can cause scar tissue that narrows the arteries further. Symptoms include shortness of breath, weakness, and chest pain.
The good news? CTEPH is one of the few forms of PH that can potentially be cured — especially when caught early. Treatment options depend on your specific situation, overall health, and where the blockages are located. Here's a breakdown:
- Pulmonary Endarterectomy (PEA): The preferred surgical treatment. It removes clots and scar tissue from the pulmonary arteries. About 4% of people don't survive the surgery, but for those who do, it can be curative. Most will need blood thinners for life afterward.
- Balloon Pulmonary Angioplasty (BPA): A less invasive option for those who can't have PEA. A small balloon widens the arteries to improve blood flow.
- Medication: Riociguat (Adempas) is currently the only FDA-approved medication for CTEPH. It's used for those who can't have surgery or still have symptoms after surgery. Other medications may also be used to manage symptoms.
- Lung Transplant: Considered a last resort when other treatments haven't worked. If CTEPH goes untreated and progresses, life expectancy can be as short as one to three years. However, surgery significantly improves outcomes — one study found PEA improves three-year survival rates to 89%, compared to 71% without surgery.
Always work closely with your care team to find the right treatment path for your specific case.
September 7
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