My PA pressure was over 100 on RHC last year.Started on Sildenafil…which I’m still on…and Opsumit.Stopped Opsumit 1 week later when it put me in hospital.Later tried Ambrisentan twice and did not tolerate that.My symptoms have increased/worsened.Started Remodulin SQ today….hoping to tolerate this and see some improvement…

Yes Uptravi helped me big time. My number was 97 severe. Last cath went down to 39. Thank God!

Mine is very high also . Dr started me on Uptravi hope it helps.

Burmawright, Hypertension is systemic and is taken with a blood pressure cuff or wrist cuff. PH is related directly to the arteries in the lungs and the right side of the heart. This is usually detected during a heart sonogram, but the definitive way is a Right Heart Cath. You can Google PAH or Pulmonary Hypertension or look at the info under Resources on this sight. My numbers are very high too. At one point, it was 79. It is still too high, but I'm still alive and kicking. I'm no Rockette, but I still try to do what I can. Hope this helps.